loading...| Preferred Name |
Dermatitis herpetiformis |
| ID |
http://www.orpha.net/ORDO/Orphanet_1656 |
| alternative_term |
Duhring-Brocq disease |
| definition |
A chronic autoimmune subepidermal bullous disease characterized by grouped pruritic lesions such as papules, urticarial plaques, erythema, and herpetiform vesiculae, with a predominantly symmetrical distribution on extensor surfaces of the elbows (90%), knees (30%), shoulders, buttocks, sacral region, and face of children and adults. Erosions, excoriations and hyperpigmentation usually follow. It may also appear as a consequence of gluten intolerance. |
| definition_citation |
Orphanet |
| expertlink |
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=en&Expert=1656 |
| has_age_of_onset |
All ages |
| has_inheritance |
Not applicable |
| hasDbXref |
ICD-11:EB44 ICD-10:L13.0 UMLS:C0011608 MedDRA:10012468 OMIM:601230 MeSH:D003874 |
| label |
Dermatitis herpetiformis |
| notation |
ORPHA:1656 |
| part_of | |
| prefixIRI |
ORDO:Orphanet_1656 |
| prefLabel |
Dermatitis herpetiformis |
| present_in |
Europe AND has_point_prevalence_average_value : 27.0 AND has_point_prevalence_range : 1-5 / 10 000 Finland AND has_point_prevalence_average_value : 75.3 AND has_point_prevalence_range : 6-9 / 10 000 United States AND has_point_prevalence_average_value : 11.2 AND has_point_prevalence_range : 1-5 / 10 000 Finland AND has_annual_incidence_average_value : 3.5 AND has_annual_incidence_range : 1-9 / 100 000 Ireland AND has_annual_incidence_average_value : 1.5 AND has_annual_incidence_range : 1-9 / 100 000 Sweden AND has_annual_incidence_average_value : 1.1 AND has_annual_incidence_range : 1-9 / 100 000 Ireland AND has_point_prevalence_average_value : 17.6 AND has_point_prevalence_range : 1-5 / 10 000 Italy AND has_annual_incidence_average_value : 0.9 AND has_annual_incidence_range : 1-9 / 1 000 000 United States AND has_annual_incidence_average_value : 0.98 AND has_annual_incidence_range : 1-9 / 1 000 000 Sweden AND has_point_prevalence_average_value : 21.0 AND has_point_prevalence_range : 1-5 / 10 000 United Kingdom AND has_point_prevalence_average_value : 11.5 AND has_point_prevalence_range : 1-5 / 10 000 |
| treeView | |
| subClassOf |