Preferred Name |
Vestibular schwannoma |
ID |
http://www.orpha.net/ORDO/Orphanet_252175 |
alternative_term |
Acoustic neurilemoma Acoustic neurinoma Acoustic neuroma |
definition |
Vestibular schwannoma is a rare tumor of the posterior fossa originating in the Schwann cells of the vestibular transitional zone of the vestibulocochlear nerve that can be benign, small, slow growing and asymptomatic or large, faster growing and aggressive and potentially fatal, presenting with symptoms of hearing and balance impairment, vertigo, ataxia, headache and fifth, sixth or seventh cranial nerve dysfunction and facial numbness. |
definition_citation |
Orphanet |
expertlink |
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=en&Expert=252175 |
hasDbXref |
ICD-11:2A02.3 MedDRA:10000523 ICD-10:D33.3 UMLS:C0027859 |
label |
Vestibular schwannoma |
notation |
Clinical subtype ORPHA:252175 |
part_of | |
prefixIRI |
ORDO:Orphanet_252175 |
prefLabel |
Vestibular schwannoma |
present_in |
United States AND has_annual_incidence_average_value : 1.2 AND has_annual_incidence_range : 1-9 / 100 000 Europe AND has_annual_incidence_range : 1-9 / 100 000 Specific population AND has_annual_incidence_average_value : 0.8 AND has_annual_incidence_range : 1-9 / 1 000 000 Denmark AND has_annual_incidence_average_value : 2.0 AND has_annual_incidence_range : 1-9 / 100 000 |
treeView | |
subClassOf |