Preferred Name |
Moyamoya Disease |
Synonyms |
Moya-Moya Disease |
Definitions |
A noninflammatory, progressive occlusion of the intracranial CAROTID ARTERIES and the formation of netlike collateral arteries arising from the CIRCLE OF WILLIS. Cerebral angiogram shows the puff-of-smoke (moyamoya) collaterals at the base of the brain. It is characterized by endothelial HYPERPLASIA and FIBROSIS with thickening of arterial walls. This disease primarily affects children but can also occur in adults. |
ID |
http://purl.bioontology.org/ontology/MESH/D009072 |
altLabel |
Moya-Moya Disease Moyamoya Syndrome Progressive Intracranial Occlusive Arteropathy (Moyamoya) Disease, Primary Moyamoya Classic Moyamoya Disease Moyamoya Disease, Secondary Secondary Moyamoya Disease Primary Moyamoya Disease Moya Moya Disease Moyamoya Diseases, Primary Disease, Classic Moyamoya Cerebrovascular Moyamoya Disease Moyamoya Disease, Primary Primary Moyamoya Diseases Disease, Moya-Moya Moyamoya Disease, Classic |
AQL |
BL CF CI CL CN CO DG DH DI DT EC EH EM EN EP ET GE HI IM ME MI MO NU PA PC PP PS PX RH RT SU TH UR VE VI |
cui |
C0751323 C0026654 C0751322 |
DC |
1 |
definition |
A noninflammatory, progressive occlusion of the intracranial CAROTID ARTERIES and the formation of netlike collateral arteries arising from the CIRCLE OF WILLIS. Cerebral angiogram shows the puff-of-smoke (moyamoya) collaterals at the base of the brain. It is characterized by endothelial HYPERPLASIA and FIBROSIS with thickening of arterial walls. This disease primarily affects children but can also occur in adults. |
DX |
19910101 |
HN |
1991(1978) |
Inverse of AQ |
http://purl.bioontology.org/ontology/MESH/Q000401 http://purl.bioontology.org/ontology/MESH/Q000150 http://purl.bioontology.org/ontology/MESH/Q000188 http://purl.bioontology.org/ontology/MESH/Q000517 http://purl.bioontology.org/ontology/MESH/Q000201 http://purl.bioontology.org/ontology/MESH/Q000145 http://purl.bioontology.org/ontology/MESH/Q000503 http://purl.bioontology.org/ontology/MESH/Q000453 http://purl.bioontology.org/ontology/MESH/Q000208 http://purl.bioontology.org/ontology/MESH/Q000134 http://purl.bioontology.org/ontology/MESH/Q000821 http://purl.bioontology.org/ontology/MESH/Q000382 http://purl.bioontology.org/ontology/MESH/Q000601 http://purl.bioontology.org/ontology/MESH/Q000235 http://purl.bioontology.org/ontology/MESH/Q000523 http://purl.bioontology.org/ontology/MESH/Q000276 http://purl.bioontology.org/ontology/MESH/Q000191 http://purl.bioontology.org/ontology/MESH/Q000652 http://purl.bioontology.org/ontology/MESH/Q000662 http://purl.bioontology.org/ontology/MESH/Q000151 http://purl.bioontology.org/ontology/MESH/Q000628 http://purl.bioontology.org/ontology/MESH/Q000196 http://purl.bioontology.org/ontology/MESH/Q000534 http://purl.bioontology.org/ontology/MESH/Q000266 http://purl.bioontology.org/ontology/MESH/Q000532 http://purl.bioontology.org/ontology/MESH/Q000139 http://purl.bioontology.org/ontology/MESH/Q000378 http://purl.bioontology.org/ontology/MESH/Q000175 http://purl.bioontology.org/ontology/MESH/Q000000981 http://purl.bioontology.org/ontology/MESH/Q000097 http://purl.bioontology.org/ontology/MESH/Q000473 http://purl.bioontology.org/ontology/MESH/Q000451 http://purl.bioontology.org/ontology/MESH/Q000209 |
Machine permutation |
1991; see ARTERIAL OCCLUSIVE DISEASES 1978-1990 |
Mapped from |
http://purl.bioontology.org/ontology/MESH/C536993 |
MDA |
19770427 |
MMR |
20120703 |
MN |
C14.907.253.560.200.737 C10.228.140.300.510.200.737 C14.907.137.615 C14.907.253.123.620 C10.228.140.300.200.600 |
notation |
D009072 |
prefLabel |
Moyamoya Disease |
TERMUI |
T369519 T369520 T369517 T027090 T369518 T027091 T369516 T369521 |
TH |
NLM (1978) NLM (2000) ORD (2010) OMIM (2013) NLM (1999) |
tui |
T047 |
subClassOf |
http://purl.bioontology.org/ontology/MESH/D002539 |