Preferred Name |
Persistent Fetal Circulation Syndrome |
Synonyms |
Persistent Pulmonary Hypertension of Newborn |
Definitions |
A syndrome of persistent PULMONARY HYPERTENSION in the newborn infant (INFANT, NEWBORN) without demonstrable HEART DISEASES. This neonatal condition can be caused by severe pulmonary vasoconstriction (reactive type), hypertrophy of pulmonary arterial muscle (hypertrophic type), or abnormally developed pulmonary arterioles (hypoplastic type). The newborn patient exhibits CYANOSIS and ACIDOSIS due to the persistence of fetal circulatory pattern of right-to-left shunting of blood through a patent ductus arteriosus (DUCTUS ARTERIOSUS, PATENT) and at times a patent foramen ovale (FORAMEN OVALE, PATENT). |
ID |
http://purl.bioontology.org/ontology/MESH/D010547 |
altLabel |
Persistent Pulmonary Hypertension of Newborn Hypertension, Pulmonary, of Newborn, Persistent Familial Persistent Pulmonary Hypertension of the Newborn Circulation, Persistent Fetal Alveolar Capillary Dysplasia With Misalignment Of Pulmonary Veins ACDMPV ACD MPV ACD-MPV Persistent Fetal Circulation Alveolar Capillary Dysplasia With Misalignment Of Pulmonary Veins And Other Congenital Anomalies Pulmonary Hypertension, Familial Persistent, of the Newborn Misalignment of the Pulmonary Vessels Fetal Circulation, Persistent |
AN |
also known as PPHN check the tags HUMANS & INFANT, NEWBORN |
AQL |
BL CF CI CL CO DG DH DI DT EC EH EM EN EP ET GE HI IM ME MI MO NU PA PC PP PS PX RH RT SU TH UR VE VI |
cui |
C0031190 |
DC |
1 |
definition |
A syndrome of persistent PULMONARY HYPERTENSION in the newborn infant (INFANT, NEWBORN) without demonstrable HEART DISEASES. This neonatal condition can be caused by severe pulmonary vasoconstriction (reactive type), hypertrophy of pulmonary arterial muscle (hypertrophic type), or abnormally developed pulmonary arterioles (hypoplastic type). The newborn patient exhibits CYANOSIS and ACIDOSIS due to the persistence of fetal circulatory pattern of right-to-left shunting of blood through a patent ductus arteriosus (DUCTUS ARTERIOSUS, PATENT) and at times a patent foramen ovale (FORAMEN OVALE, PATENT). |
DX |
19800101 |
FX |
D004374 |
HN |
1980 |
Inverse of AQ |
http://purl.bioontology.org/ontology/MESH/Q000401 http://purl.bioontology.org/ontology/MESH/Q000150 http://purl.bioontology.org/ontology/MESH/Q000188 http://purl.bioontology.org/ontology/MESH/Q000517 http://purl.bioontology.org/ontology/MESH/Q000201 http://purl.bioontology.org/ontology/MESH/Q000145 http://purl.bioontology.org/ontology/MESH/Q000503 http://purl.bioontology.org/ontology/MESH/Q000453 http://purl.bioontology.org/ontology/MESH/Q000208 http://purl.bioontology.org/ontology/MESH/Q000134 http://purl.bioontology.org/ontology/MESH/Q000821 http://purl.bioontology.org/ontology/MESH/Q000382 http://purl.bioontology.org/ontology/MESH/Q000601 http://purl.bioontology.org/ontology/MESH/Q000235 http://purl.bioontology.org/ontology/MESH/Q000523 http://purl.bioontology.org/ontology/MESH/Q000276 http://purl.bioontology.org/ontology/MESH/Q000191 http://purl.bioontology.org/ontology/MESH/Q000652 http://purl.bioontology.org/ontology/MESH/Q000662 http://purl.bioontology.org/ontology/MESH/Q000628 http://purl.bioontology.org/ontology/MESH/Q000196 http://purl.bioontology.org/ontology/MESH/Q000534 http://purl.bioontology.org/ontology/MESH/Q000266 http://purl.bioontology.org/ontology/MESH/Q000532 http://purl.bioontology.org/ontology/MESH/Q000139 http://purl.bioontology.org/ontology/MESH/Q000378 http://purl.bioontology.org/ontology/MESH/Q000175 http://purl.bioontology.org/ontology/MESH/Q000000981 http://purl.bioontology.org/ontology/MESH/Q000097 http://purl.bioontology.org/ontology/MESH/Q000473 http://purl.bioontology.org/ontology/MESH/Q000451 http://purl.bioontology.org/ontology/MESH/Q000209 |
Inverse of RO | |
Machine permutation |
1980 |
Mapped from | |
MDA |
19790228 |
MMR |
20130708 |
MN |
C08.381.423.694 C16.614.694 |
notation |
D010547 |
prefLabel |
Persistent Fetal Circulation Syndrome |
TERMUI |
T811822 T031139 T840884 T753016 T811823 T031140 T843554 T031142 T031141 T031138 T031143 T843553 T840885 |
TH |
NLM (1980) UNK (19XX) NLM (1994) NLM (2010) ORD (2010) OMIM (2013) GHR (2014) |
tui |
T047 |
subClassOf |