Preferred Name |
Congenitally corrected transposition of the great arteries |
ID |
http://www.orpha.net/ORDO/Orphanet_216694 |
alternative_term |
L-transposition of the great arteries Congenitally corrected transposition of the great vessels Discordant ventriculoarterial and atrioventricular connections Ventriculoarterial and atrioventricular discordance Ventricular inversion Levo-transposition of the great arteries Double discordance |
definition |
Congenitally corrected transposition (CCT) of the great vessels is a rare cardiac malformation characterized by the combination of discordant atrioventricular and ventriculo-arterial connections, usually accompanied by other cardiovascular malformations. |
definition_citation |
Orphanet |
expertlink |
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=en&Expert=216694 |
has_age_of_onset |
All ages |
has_inheritance |
Not applicable |
hasDbXref |
MedDRA:10011120 ICD-11:LA85.00 UMLS:C0344616 MeSH:C535426 ICD-10:Q20.5 |
label |
Congenitally corrected transposition of the great arteries |
notation |
ORPHA:216694 |
part_of | |
prefixIRI |
ORDO:Orphanet_216694 |
prefLabel |
Congenitally corrected transposition of the great arteries |
present_in |
Worldwide AND has_point_prevalence_range : Unknown Worldwide AND has_birth_prevalence_average_value : 3.0 AND has_birth_prevalence_range : 1-9 / 100 000 |
treeView | |
subClassOf |