| Preferred Name |
gamma-Butyrobetaine Dioxygenase |
| Synonyms |
Trimethylaminobutyrate Hydroxylase |
| Definitions |
An enzyme that catalyzes the HYDROXYLATION of gamma-butyrobetaine to L-CARNITINE. It is the last enzyme in the biosynthetic pathway of L-CARNITINE and is dependent on alpha-ketoglutarate; IRON; ASCORBIC ACID; and OXYGEN. |
| ID |
http://purl.bioontology.org/ontology/MESH/D050563 |
| altLabel |
Trimethylaminobutyrate Hydroxylase Hydroxylase, Butyrobetaine Dioxygenase, gamma-Butyrobetaine gamma-Butyrobetaine,2-Oxoglutarate Dioxygenase gamma-Butyrobetaine, 2-Oxoglutarate Dioxygenase gamma Butyrobetaine,2 Oxoglutarate Dioxygenase Hydroxylase, Trimethylaminobutyrate Dioxygenase gamma-Butyrobetaine, 2-Oxoglutarate gamma Butyrobetaine, 2 Oxoglutarate Dioxygenase Dioxygenase, gamma-Butyrobetaine,2-Oxoglutarate 4-Trimethylaminobutyrate, 2-Oxoglutarate Oxygen Oxidoreductase (3-Hydroxylating) gamma-Butyrobetaine Hydroxylase Hydroxylase, gamma-Butyrobetaine 2-Oxoglutarate Dioxygenase gamma-Butyrobetaine gamma Butyrobetaine Hydroxylase gamma Butyrobetaine Dioxygenase Butyrobetaine Hydroxylase |
| AQL |
AD AE AI AN BI BL CF CH CL CS DE DF EC GE HI IM IP ME PD PH PK PO RE SD ST TO TU UL UR |
| cui |
C0061031 |
| DC |
1 |
| definition |
An enzyme that catalyzes the HYDROXYLATION of gamma-butyrobetaine to L-CARNITINE. It is the last enzyme in the biosynthetic pathway of L-CARNITINE and is dependent on alpha-ketoglutarate; IRON; ASCORBIC ACID; and OXYGEN. |
| DX |
20060101 |
| HN |
2006(1980); use KETOGLUTARIC ACID 1973-1974, BETAINE 1972-1979, BUTYRATES 1974-1979, & AMINOBUTYRIC ACID 1970-1974 |
| Inverse of AQ |
http://purl.bioontology.org/ontology/MESH/Q000032 http://purl.bioontology.org/ontology/MESH/Q000138 http://purl.bioontology.org/ontology/MESH/Q000737 http://purl.bioontology.org/ontology/MESH/Q000493 http://purl.bioontology.org/ontology/MESH/Q000145 http://purl.bioontology.org/ontology/MESH/Q000506 http://purl.bioontology.org/ontology/MESH/Q000187 http://purl.bioontology.org/ontology/MESH/Q000096 http://purl.bioontology.org/ontology/MESH/Q000037 http://purl.bioontology.org/ontology/MESH/Q000134 http://purl.bioontology.org/ontology/MESH/Q000592 http://purl.bioontology.org/ontology/MESH/Q000528 http://purl.bioontology.org/ontology/MESH/Q000008 http://purl.bioontology.org/ontology/MESH/Q000235 http://purl.bioontology.org/ontology/MESH/Q000648 http://purl.bioontology.org/ontology/MESH/Q000276 http://purl.bioontology.org/ontology/MESH/Q000191 http://purl.bioontology.org/ontology/MESH/Q000633 http://purl.bioontology.org/ontology/MESH/Q000652 http://purl.bioontology.org/ontology/MESH/Q000009 http://purl.bioontology.org/ontology/MESH/Q000302 http://purl.bioontology.org/ontology/MESH/Q000502 http://purl.bioontology.org/ontology/MESH/Q000494 http://purl.bioontology.org/ontology/MESH/Q000266 http://purl.bioontology.org/ontology/MESH/Q000600 http://purl.bioontology.org/ontology/MESH/Q000378 http://purl.bioontology.org/ontology/MESH/Q000172 |
| Inverse of RB |
EC 1.14.11.1 |
| Machine permutation |
2006; GAMMA-BUTYROBETAINE DIOXYGENASE was indexed under MIXED FUNCTION OXYGENASES 1980-2005, KETOGLUTARIC ACID 1973-1974, BETAINE 1972-1980, BUTYRATES 1974-1979, & AMINOBUTYRIC ACID 1970-1974 |
| Mapped from | |
| MDA |
20050630 |
| MN |
D08.811.682.690.708.401 |
| notation |
D050563 |
| prefLabel |
gamma-Butyrobetaine Dioxygenase |
| TERMUI |
T630677 T102680 T102676 T102678 T102677 T629666 T102679 |
| TH |
NLM (2006) |
| tui |
T116 T126 |
| subClassOf |
| Delete | Mapping To | Ontology | Source |
|---|---|---|---|
| http://purl.obolibrary.org/obo/PR_000004662 | Protein Ontology / 蛋白质本体 | LOOM |