| Preferred Name |
Glutaryl-CoA Dehydrogenase |
| Synonyms |
Dehydrogenase, Glutaryl-CoA |
| Definitions |
A flavoprotein enzyme that is responsible for the catabolism of LYSINE; HYDROXYLYSINE; and TRYPTOPHAN. It catalyzes the oxidation of GLUTARYL-CoA to crotonoyl-CoA using FAD as a cofactor. Glutaric aciduria type I is an inborn error of metabolism due to the deficiency of glutaryl-CoA dehydrogenase. |
| ID |
http://purl.bioontology.org/ontology/MESH/D050770 |
| altLabel |
Dehydrogenase, Glutaryl-CoA Glutaryl Coenzyme A Dehydrogenase Glutaryl-Coenzyme A Dehydrogenase Dehydrogenase, Glutaryl CoA Glutaryl CoA Dehydrogenase CoA Dehydrogenase, Glutaryl Dehydrogenase, Glutaryl-Coenzyme A |
| AQL |
AD AE AI AN BI BL CF CH CL CS DE DF EC GE HI IM IP ME PD PH PK PO RE SD ST TO TU UL UR |
| cui |
C0061510 |
| DC |
1 |
| definition |
A flavoprotein enzyme that is responsible for the catabolism of LYSINE; HYDROXYLYSINE; and TRYPTOPHAN. It catalyzes the oxidation of GLUTARYL-CoA to crotonoyl-CoA using FAD as a cofactor. Glutaric aciduria type I is an inborn error of metabolism due to the deficiency of glutaryl-CoA dehydrogenase. |
| DX |
20060101 |
| HN |
2006(1973) |
| Inverse of AQ |
http://purl.bioontology.org/ontology/MESH/Q000032 http://purl.bioontology.org/ontology/MESH/Q000138 http://purl.bioontology.org/ontology/MESH/Q000737 http://purl.bioontology.org/ontology/MESH/Q000493 http://purl.bioontology.org/ontology/MESH/Q000145 http://purl.bioontology.org/ontology/MESH/Q000506 http://purl.bioontology.org/ontology/MESH/Q000187 http://purl.bioontology.org/ontology/MESH/Q000096 http://purl.bioontology.org/ontology/MESH/Q000037 http://purl.bioontology.org/ontology/MESH/Q000134 http://purl.bioontology.org/ontology/MESH/Q000592 http://purl.bioontology.org/ontology/MESH/Q000528 http://purl.bioontology.org/ontology/MESH/Q000008 http://purl.bioontology.org/ontology/MESH/Q000235 http://purl.bioontology.org/ontology/MESH/Q000648 http://purl.bioontology.org/ontology/MESH/Q000276 http://purl.bioontology.org/ontology/MESH/Q000191 http://purl.bioontology.org/ontology/MESH/Q000633 http://purl.bioontology.org/ontology/MESH/Q000652 http://purl.bioontology.org/ontology/MESH/Q000009 http://purl.bioontology.org/ontology/MESH/Q000302 http://purl.bioontology.org/ontology/MESH/Q000502 http://purl.bioontology.org/ontology/MESH/Q000494 http://purl.bioontology.org/ontology/MESH/Q000266 http://purl.bioontology.org/ontology/MESH/Q000600 http://purl.bioontology.org/ontology/MESH/Q000378 http://purl.bioontology.org/ontology/MESH/Q000172 |
| Inverse of RB |
EC 1.3.8.6 |
| Machine permutation |
2006; GLUTARYL-COA DEHYDROGENASE was indexed under ACYL COENZYME A 1973-1979; under GLUTARATES 1973-1982; and under COENZYME A 1973-1979; under OXIDOREDUCTASES ACTING ON CH-CH GROUP DONORS 2004-2005 |
| Mapped from | |
| MDA |
20050630 |
| MMR |
20130708 |
| MN |
D08.811.682.660.425 |
| notation |
D050770 |
| prefLabel |
Glutaryl-CoA Dehydrogenase |
| RR |
37255-38-2 (CRN) |
| TERMUI |
T104615 T104616 T104617 |
| TH |
NLM (2006) |
| tui |
T116 T126 |
| subClassOf |