Preferred Name

Hypereosinophilic syndrome

ID

http://www.orpha.net/ORDO/Orphanet_168956

alternative_term

HES

definition

Hypereosinophilic syndrome (HES) constitutes a rare and heterogeneous group of disorders, defined as persistent and marked blood eosinophilia and/or tissue eosinophilia associated with a wide range of clinical manifestations reflecting eosinophil-induced tissue/organ damage.

definition_citation

Orphanet

expertlink

https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=en&Expert=168956

has_age_of_onset

All ages

has_inheritance

Unknown

Not applicable

hasDbXref

MedDRA:10048643

UMLS:C1540912

MeSH:D017681

label

Hypereosinophilic syndrome

notation

Clinical group

ORPHA:168956

prefixIRI

ORDO:Orphanet_168956

prefLabel

Hypereosinophilic syndrome

present_in

Europe AND has_point_prevalence_range : Unknown

Europe AND has_annual_incidence_range : <1 / 1 000 000

United States AND has_annual_incidence_average_value : 0.027 AND has_annual_incidence_range : <1 / 1 000 000

United States AND has_point_prevalence_average_value : 3.3 AND has_point_prevalence_range : 1-9 / 100 000

subClassOf

http://www.orpha.net/ORDO/Orphanet_98274

http://www.orpha.net/ORDO/Orphanet_217720

http://www.orpha.net/ORDO/Orphanet_557492

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Delete Mapping To Ontology Source
http://purl.obolibrary.org/obo/DOID_999 BioAssay Ontology / 生物活性分析本体 LOOM
http://purl.obolibrary.org/obo/DOID_999 Ontology of Drug Adverse Events / 药物不良反应本体 LOOM
http://purl.obolibrary.org/obo/DOID_999 Human Disease Ontology / 人类疾病本体 LOOM
http://purl.obolibrary.org/obo/MONDO_0015691 Mondo Disease Ontology / Mondo疾病本体 LOOM
http://purl.bioontology.org/ontology/MESH/D017681 Medical Subject Headings / 医学主题词表 LOOM
http://www.ebi.ac.uk/efo/EFO_1001467 Experimental Factor Ontology / 实验性因素本体 LOOM
http://purl.bioontology.org/ontology/MEDLINEPLUS/C1540912 MedlinePlus Health Topics / MedlinePlus网站健康主题 LOOM