| Preferred Name |
Hypereosinophilic syndrome |
| ID |
http://www.orpha.net/ORDO/Orphanet_168956 |
| alternative_term |
HES |
| definition |
Hypereosinophilic syndrome (HES) constitutes a rare and heterogeneous group of disorders, defined as persistent and marked blood eosinophilia and/or tissue eosinophilia associated with a wide range of clinical manifestations reflecting eosinophil-induced tissue/organ damage. |
| definition_citation |
Orphanet |
| expertlink |
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=en&Expert=168956 |
| has_age_of_onset |
All ages |
| has_inheritance |
Unknown Not applicable |
| hasDbXref |
MedDRA:10048643 UMLS:C1540912 MeSH:D017681 |
| label |
Hypereosinophilic syndrome |
| notation |
Clinical group ORPHA:168956 |
| prefixIRI |
ORDO:Orphanet_168956 |
| prefLabel |
Hypereosinophilic syndrome |
| present_in |
Europe AND has_point_prevalence_range : Unknown Europe AND has_annual_incidence_range : <1 / 1 000 000 United States AND has_annual_incidence_average_value : 0.027 AND has_annual_incidence_range : <1 / 1 000 000 United States AND has_point_prevalence_average_value : 3.3 AND has_point_prevalence_range : 1-9 / 100 000 |
| subClassOf |
http://www.orpha.net/ORDO/Orphanet_98274 |