| Preferred Name |
Rheumatic fever |
| ID |
http://www.orpha.net/ORDO/Orphanet_3099 |
| alternative_term |
Acute rheumatic fever |
| definition |
Rheumatic fever (RF) is a multisystem inflammatory disease occurring as a post-infectious, nonsuppurative sequela of untreated streptococcus pyogenes (Group A streptococcus [GAS]) pharyngitis, and mainly occurs in individuals aged 5 to 15 years. The most common presenting signs are fever, migratory polyarthritis and carditis. |
| definition_citation |
Orphanet |
| expertlink |
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=en&Expert=3099 |
| has_age_of_onset |
Childhood |
| has_inheritance |
Not applicable |
| hasDbXref |
ICD-10:I01.2 ICD-11:1B41 ICD-10:I01.0 MedDRA:10039054 UMLS:C0035436 ICD-10:I00 ICD-11:1B40 ICD-10:I01.1 ICD-10:I01.9 MeSH:D012213 ICD-10:I01.8 OMIM:268240 |
| label |
Rheumatic fever |
| notation |
ORPHA:3099 |
| part_of | |
| prefixIRI |
ORDO:Orphanet_3099 |
| prefLabel |
Rheumatic fever |
| present_in |
Worldwide AND has_point_prevalence_range : Unknown Latin America AND has_annual_incidence_average_value : 5.0 AND has_annual_incidence_range : 1-9 / 100 000 New Zealand AND has_annual_incidence_average_value : 7.6 AND has_annual_incidence_range : 1-9 / 100 000 Canada AND has_annual_incidence_average_value : 12.5 AND has_annual_incidence_range : 1-5 / 10 000 India AND has_annual_incidence_average_value : 30.0 AND has_annual_incidence_range : 1-5 / 10 000 Mexico AND has_annual_incidence_average_value : 100.0 AND has_annual_incidence_range : >1 / 1000 Europe AND has_annual_incidence_average_value : 5.0 AND has_annual_incidence_range : 1-9 / 100 000 Spain AND has_annual_incidence_average_value : 12.5 AND has_annual_incidence_range : 1-5 / 10 000 Australia AND has_annual_incidence_average_value : 100.0 AND has_annual_incidence_range : >1 / 1000 |
| treeView | |
| subClassOf |