Preferred Name

Rheumatic fever

ID

http://www.orpha.net/ORDO/Orphanet_3099

alternative_term

Acute rheumatic fever

definition

Rheumatic fever (RF) is a multisystem inflammatory disease occurring as a post-infectious, nonsuppurative sequela of untreated streptococcus pyogenes (Group A streptococcus [GAS]) pharyngitis, and mainly occurs in individuals aged 5 to 15 years. The most common presenting signs are fever, migratory polyarthritis and carditis.

definition_citation

Orphanet

expertlink

https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=en&Expert=3099

has_age_of_onset

Childhood

has_inheritance

Not applicable

hasDbXref

ICD-10:I01.2

ICD-11:1B41

ICD-10:I01.0

MedDRA:10039054

UMLS:C0035436

ICD-10:I00

ICD-11:1B40

ICD-10:I01.1

ICD-10:I01.9

MeSH:D012213

ICD-10:I01.8

OMIM:268240

label

Rheumatic fever

notation

ORPHA:3099

part_of

http://www.orpha.net/ORDO/Orphanet_182222

prefixIRI

ORDO:Orphanet_3099

prefLabel

Rheumatic fever

present_in

Worldwide AND has_point_prevalence_range : Unknown

Latin America AND has_annual_incidence_average_value : 5.0 AND has_annual_incidence_range : 1-9 / 100 000

New Zealand AND has_annual_incidence_average_value : 7.6 AND has_annual_incidence_range : 1-9 / 100 000

Canada AND has_annual_incidence_average_value : 12.5 AND has_annual_incidence_range : 1-5 / 10 000

India AND has_annual_incidence_average_value : 30.0 AND has_annual_incidence_range : 1-5 / 10 000

Mexico AND has_annual_incidence_average_value : 100.0 AND has_annual_incidence_range : >1 / 1000

Europe AND has_annual_incidence_average_value : 5.0 AND has_annual_incidence_range : 1-9 / 100 000

Spain AND has_annual_incidence_average_value : 12.5 AND has_annual_incidence_range : 1-5 / 10 000

Australia AND has_annual_incidence_average_value : 100.0 AND has_annual_incidence_range : >1 / 1000

treeView

http://www.orpha.net/ORDO/Orphanet_182222

subClassOf

http://www.orpha.net/ORDO/Orphanet_377788

http://www.orpha.net/ORDO/Orphanet_557493

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