Preferred Name

Takayasu arteritis

ID

http://www.orpha.net/ORDO/Orphanet_3287

definition

A rare predominantly large-vessel vasculitis that is characterized by affected aorta and its major branches, but also other large vessels, causing stenosis, occlusion, or aneurysm.

definition_citation

Orphanet

expertlink

https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=en&Expert=3287

has_age_of_onset

Adult

Adolescent

has_inheritance

Not applicable

hasDbXref

UMLS:C0039263

MeSH:D013625

OMIM:207600

ICD-10:M31.4

ICD-11:4A44.1

MedDRA:10043097

label

Takayasu arteritis

notation

ORPHA:3287

part_of

http://www.orpha.net/ORDO/Orphanet_567560

http://www.orpha.net/ORDO/Orphanet_280369

http://www.orpha.net/ORDO/Orphanet_156140

prefixIRI

ORDO:Orphanet_3287

prefLabel

Takayasu arteritis

present_in

Poland AND has_point_prevalence_average_value : 0.46 AND has_point_prevalence_range : 1-9 / 1 000 000

Norway AND has_point_prevalence_average_value : 2.56 AND has_point_prevalence_range : 1-9 / 100 000

Japan AND has_point_prevalence_average_value : 4.0 AND has_point_prevalence_range : 1-9 / 100 000

Germany AND has_annual_incidence_average_value : 0.07 AND has_annual_incidence_range : <1 / 1 000 000

Europe AND has_point_prevalence_average_value : 1.34 AND has_point_prevalence_range : 1-9 / 100 000

Japan AND has_annual_incidence_average_value : 0.15 AND has_annual_incidence_range : 1-9 / 1 000 000

Europe AND has_annual_incidence_average_value : 0.084 AND has_annual_incidence_range : <1 / 1 000 000

United States AND has_annual_incidence_average_value : 0.26 AND has_annual_incidence_range : 1-9 / 1 000 000

Korea, Republic of AND has_annual_incidence_average_value : 0.24 AND has_annual_incidence_range : 1-9 / 1 000 000

Norway AND has_annual_incidence_average_value : 0.15 AND has_annual_incidence_range : 1-9 / 1 000 000

Kuwait AND has_annual_incidence_average_value : 0.22 AND has_annual_incidence_range : 1-9 / 1 000 000

United Kingdom AND has_point_prevalence_average_value : 0.47 AND has_point_prevalence_range : 1-9 / 1 000 000

Denmark AND has_annual_incidence_average_value : 0.04 AND has_annual_incidence_range : <1 / 1 000 000

Kuwait AND has_point_prevalence_average_value : 0.78 AND has_point_prevalence_range : 1-9 / 1 000 000

Lithuania AND has_annual_incidence_average_value : 0.13 AND has_annual_incidence_range : 1-9 / 1 000 000

Worldwide AND has_point_prevalence_range : 1-9 / 100 000

Sweden AND has_point_prevalence_average_value : 0.98 AND has_point_prevalence_range : 1-9 / 1 000 000

United Kingdom AND has_annual_incidence_average_value : 0.06 AND has_annual_incidence_range : <1 / 1 000 000

Korea, Republic of AND has_point_prevalence_average_value : 2.82 AND has_point_prevalence_range : 1-9 / 100 000

Sweden AND has_annual_incidence_average_value : 0.1 AND has_annual_incidence_range : 1-9 / 1 000 000

Poland AND has_annual_incidence_average_value : 0.092 AND has_annual_incidence_range : <1 / 1 000 000

treeView

http://www.orpha.net/ORDO/Orphanet_567560

http://www.orpha.net/ORDO/Orphanet_280369

http://www.orpha.net/ORDO/Orphanet_156140

subClassOf

http://www.orpha.net/ORDO/Orphanet_377788

http://www.orpha.net/ORDO/Orphanet_557493

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Delete Mapping To Ontology Source
http://purl.bioontology.org/ontology/MESH/D013625 Medical Subject Headings / 医学主题词表 LOOM
http://purl.bioontology.org/ontology/OMIM/207600 Online Mendelian Inheritance in Man / 在线人类孟德尔遗传数据库 LOOM
http://www.ebi.ac.uk/efo/EFO_1001857 Experimental Factor Ontology / 实验性因素本体 LOOM
http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C35062 National Cancer Institute Thesaurus / 美国国家癌症研究所词典 LOOM
http://purl.obolibrary.org/obo/MONDO_0017991 Mondo Disease Ontology / Mondo疾病本体 LOOM