| Preferred Name |
Takayasu arteritis |
| ID |
http://www.orpha.net/ORDO/Orphanet_3287 |
| definition |
A rare predominantly large-vessel vasculitis that is characterized by affected aorta and its major branches, but also other large vessels, causing stenosis, occlusion, or aneurysm. |
| definition_citation |
Orphanet |
| expertlink |
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=en&Expert=3287 |
| has_age_of_onset |
Adult Adolescent |
| has_inheritance |
Not applicable |
| hasDbXref |
UMLS:C0039263 MeSH:D013625 OMIM:207600 ICD-10:M31.4 ICD-11:4A44.1 MedDRA:10043097 |
| label |
Takayasu arteritis |
| notation |
ORPHA:3287 |
| part_of |
http://www.orpha.net/ORDO/Orphanet_567560 |
| prefixIRI |
ORDO:Orphanet_3287 |
| prefLabel |
Takayasu arteritis |
| present_in |
Poland AND has_point_prevalence_average_value : 0.46 AND has_point_prevalence_range : 1-9 / 1 000 000 Norway AND has_point_prevalence_average_value : 2.56 AND has_point_prevalence_range : 1-9 / 100 000 Japan AND has_point_prevalence_average_value : 4.0 AND has_point_prevalence_range : 1-9 / 100 000 Germany AND has_annual_incidence_average_value : 0.07 AND has_annual_incidence_range : <1 / 1 000 000 Europe AND has_point_prevalence_average_value : 1.34 AND has_point_prevalence_range : 1-9 / 100 000 Japan AND has_annual_incidence_average_value : 0.15 AND has_annual_incidence_range : 1-9 / 1 000 000 Europe AND has_annual_incidence_average_value : 0.084 AND has_annual_incidence_range : <1 / 1 000 000 United States AND has_annual_incidence_average_value : 0.26 AND has_annual_incidence_range : 1-9 / 1 000 000 Korea, Republic of AND has_annual_incidence_average_value : 0.24 AND has_annual_incidence_range : 1-9 / 1 000 000 Norway AND has_annual_incidence_average_value : 0.15 AND has_annual_incidence_range : 1-9 / 1 000 000 Kuwait AND has_annual_incidence_average_value : 0.22 AND has_annual_incidence_range : 1-9 / 1 000 000 United Kingdom AND has_point_prevalence_average_value : 0.47 AND has_point_prevalence_range : 1-9 / 1 000 000 Denmark AND has_annual_incidence_average_value : 0.04 AND has_annual_incidence_range : <1 / 1 000 000 Kuwait AND has_point_prevalence_average_value : 0.78 AND has_point_prevalence_range : 1-9 / 1 000 000 Lithuania AND has_annual_incidence_average_value : 0.13 AND has_annual_incidence_range : 1-9 / 1 000 000 Worldwide AND has_point_prevalence_range : 1-9 / 100 000 Sweden AND has_point_prevalence_average_value : 0.98 AND has_point_prevalence_range : 1-9 / 1 000 000 United Kingdom AND has_annual_incidence_average_value : 0.06 AND has_annual_incidence_range : <1 / 1 000 000 Korea, Republic of AND has_point_prevalence_average_value : 2.82 AND has_point_prevalence_range : 1-9 / 100 000 Sweden AND has_annual_incidence_average_value : 0.1 AND has_annual_incidence_range : 1-9 / 1 000 000 Poland AND has_annual_incidence_average_value : 0.092 AND has_annual_incidence_range : <1 / 1 000 000 |
| treeView |
http://www.orpha.net/ORDO/Orphanet_567560 |
| subClassOf |