loading...| Preferred Name |
Plasmacytoma |
| ID |
http://www.orpha.net/ORDO/Orphanet_86855 |
| alternative_term |
Solitary plasmacytoma |
| definition |
Plasmacytoma is a localized mass of neoplastic monoclonal plasma cells that represents approximately 5% of all plasma cell neoplasms. There are two separate entities: primary plasmacytoma of the bone and extramedullary plasmacytoma of the soft tissues. Of the extramedullary plasmacytomas, 80% occur in the head and neck, usually in the upper respiratory tract. The median age at diagnosis is 50 years and the male to female ratio is 3:1. Long-term survival is possible following local radiotherapy, particularly for soft tissue presentations. |
| definition_citation |
Orphanet |
| expertlink |
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=en&Expert=86855 |
| has_age_of_onset |
Adult |
| has_inheritance |
Not applicable |
| hasDbXref |
UMLS:C0032131 MedDRA:10035484 ICD-10:C90.2 MeSH:D010954 ICD-11:2A83.2 ICD-10:C90.3 |
| label |
Plasmacytoma |
| notation |
ORPHA:86855 |
| part_of | |
| prefixIRI |
ORDO:Orphanet_86855 |
| prefLabel |
Plasmacytoma |
| present_in |
Worldwide AND has_point_prevalence_range : Unknown United States AND has_annual_incidence_average_value : 0.34 AND has_annual_incidence_range : 1-9 / 1 000 000 |
| treeView | |
| subClassOf |