An almost always malignant GLUCAGON-secreting tumor derived from the PANCREATIC ALPHA CELLS. It is characterized by a distinctive migratory ERYTHEMA; WEIGHT LOSS; STOMATITIS; GLOSSITIS; DIABETES MELLITUS; hypoaminoacidemia; and normochromic normocytic ANEMIA.
ID
http://purl.bioontology.org/ontology/MESH/D005935
altLabel
Adenoma, alpha-Cell
alpha-Cell Tumor
Syndrome, Glucagonoma
alpha-Cell Adenoma
Adenoma, alpha Cell
Tumor, alpha-Cell
alpha-Cell Adenomas
Tumors, alpha-Cell
Glucagonomas
Adenomas, alpha-Cell
alpha-Cell Tumors
Glucagonoma Syndromes
Glucagonoma Syndrome
Syndromes, Glucagonoma
alpha Cell Tumor
AN
coordinate IM with PANCREATIC NEOPLASMS (IM); for glucagonoma syndrome, coordinate also with NECROLYTIC MIGRATORY ERYTHEMA
AQL
BL BS CF CH CI CL CN CO DG DH DI DT EC EH EM EN EP ET GE HI IM ME MI MO NU PA PC PP PS PX RH RT SC SU TH UL UR VE VI
cui
C0017689
DC
1
definition
An almost always malignant GLUCAGON-secreting tumor derived from the PANCREATIC ALPHA CELLS. It is characterized by a distinctive migratory ERYTHEMA; WEIGHT LOSS; STOMATITIS; GLOSSITIS; DIABETES MELLITUS; hypoaminoacidemia; and normochromic normocytic ANEMIA.
DX
19910101
FX
D058568
HN
91(82); was see under ISLET CELL TUMOR 1982-90; was see ISLET CELL TUMOR 1981