| Preferred Name |
Kawasaki disease |
| ID |
http://www.orpha.net/ORDO/Orphanet_2331 |
| alternative_term |
Mucocutaneous lymph node syndrome |
| definition |
A rare inflammatory disease characterized by an acute febrile, systemic, self-limiting, medium-vessel vasculitis primarily affecting children. It often causes acute coronary arteritis which is associated with coronary arterial aneurysms (CAA) that may be life threatening when untreated. |
| definition_citation |
Orphanet |
| expertlink |
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=en&Expert=2331 |
| has_age_of_onset |
Adult Adolescent Childhood Infancy |
| has_inheritance |
Multigenic/multifactorial |
| hasDbXref |
ICD-11:4A44.5 MedDRA:10023320 UMLS:C0026691 ICD-10:M30.3 OMIM:611775 |
| label |
Kawasaki disease |
| notation |
ORPHA:2331 |
| part_of | |
| prefixIRI |
ORDO:Orphanet_2331 |
| prefLabel |
Kawasaki disease |
| present_in |
Worldwide AND has_point_prevalence_range : Unknown |
| treeView | |
| subClassOf |