Preferred Name

Tularemia

ID

http://www.orpha.net/ORDO/Orphanet_3392

definition

A rare bacterial infectious disease caused by Francisella tularensis and characterized by six major clinical presentations: ulceroglandular, glandular, oropharyngeal, oculoglandular, pneumonic, or typhoidal, depending on the route of infection. Early flu-like symptoms are common to all forms and are accompanied/followed by either a skin inoculation ulcer with localized lymphadenopathy; isolated lymphadenopathy; chronic pharyngitis with cervical lymphadenopathy; conjunctivitis with localized lymphadenopathy; lung involvement; severe systemic disease with neurological symptoms.

definition_citation

Orphanet

expertlink

https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=en&Expert=3392

has_age_of_onset

All ages

has_inheritance

Not applicable

hasDbXref

ICD-10:A21.1

ICD-10:A21.9

ICD-10:A21.0

ICD-11:1B94.Y

UMLS:C0041351

ICD-10:A21.2

MeSH:D014406

ICD-10:A21.3

ICD-10:A21.8

ICD-10:A21.7

MedDRA:10045146

ICD-11:1B94

ICD-11:1B94.0

label

Tularemia

notation

ORPHA:3392

part_of

http://www.orpha.net/ORDO/Orphanet_163582

prefixIRI

ORDO:Orphanet_3392

prefLabel

Tularemia

present_in

Slovenia AND has_annual_incidence_average_value : 0.01 AND has_annual_incidence_range : <1 / 1 000 000

France AND has_annual_incidence_average_value : 0.08 AND has_annual_incidence_range : <1 / 1 000 000

Latvia AND has_annual_incidence_average_value : 0.145 AND has_annual_incidence_range : 1-9 / 1 000 000

Bulgaria AND has_annual_incidence_average_value : 0.6 AND has_annual_incidence_range : 1-9 / 1 000 000

Europe AND has_annual_incidence_average_value : 0.2 AND has_annual_incidence_range : 1-9 / 1 000 000

Czech Republic AND has_annual_incidence_average_value : 1.27 AND has_annual_incidence_range : 1-9 / 100 000

Romania AND has_annual_incidence_average_value : 0.01 AND has_annual_incidence_range : <1 / 1 000 000

Norway AND has_annual_incidence_average_value : 1.83 AND has_annual_incidence_range : 1-9 / 100 000

Spain AND has_annual_incidence_average_value : 0.75 AND has_annual_incidence_range : 1-9 / 1 000 000

Lithuania AND has_annual_incidence_average_value : 0.07 AND has_annual_incidence_range : <1 / 1 000 000

Finland AND has_annual_incidence_average_value : 9.1 AND has_annual_incidence_range : 1-9 / 100 000

Netherlands AND has_annual_incidence_range : <1 / 1 000 000

Denmark AND has_annual_incidence_average_value : 0.05 AND has_annual_incidence_range : <1 / 1 000 000

Hungary AND has_annual_incidence_average_value : 0.5 AND has_annual_incidence_range : 1-9 / 1 000 000

Estonia AND has_annual_incidence_average_value : 0.075 AND has_annual_incidence_range : <1 / 1 000 000

Sweden AND has_annual_incidence_average_value : 4.0 AND has_annual_incidence_range : 1-9 / 100 000

Austria AND has_annual_incidence_average_value : 0.1 AND has_annual_incidence_range : 1-9 / 1 000 000

Europe AND has_point_prevalence_average_value : 2.0 AND has_point_prevalence_range : 1-9 / 100 000

Italy AND has_annual_incidence_average_value : 0.035 AND has_annual_incidence_range : <1 / 1 000 000

United Kingdom AND has_annual_incidence_range : <1 / 1 000 000

Switzerland AND has_annual_incidence_average_value : 0.25 AND has_annual_incidence_range : 1-9 / 1 000 000

Croatia AND has_annual_incidence_average_value : 0.3 AND has_annual_incidence_range : 1-9 / 1 000 000

Belgium AND has_annual_incidence_average_value : 0.005 AND has_annual_incidence_range : <1 / 1 000 000

Germany AND has_annual_incidence_average_value : 0.02 AND has_annual_incidence_range : <1 / 1 000 000

Poland AND has_annual_incidence_average_value : 0.01 AND has_annual_incidence_range : <1 / 1 000 000

Slovakia AND has_annual_incidence_average_value : 0.1 AND has_annual_incidence_range : 1-9 / 1 000 000

treeView

http://www.orpha.net/ORDO/Orphanet_163582

subClassOf

http://www.orpha.net/ORDO/Orphanet_377788

http://www.orpha.net/ORDO/Orphanet_557493

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Delete Mapping To Ontology Source
http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C85208 National Cancer Institute Thesaurus / 美国国家癌症研究所词典 LOOM
http://purl.bioontology.org/ontology/MEDLINEPLUS/C0041351 MedlinePlus Health Topics / MedlinePlus网站健康主题 LOOM
http://purl.bioontology.org/ontology/LNC/LA10514-0 Logical Observation Identifier Names and Codes / 逻辑观察标识符名称和代码 LOOM
http://purl.bioontology.org/ontology/MESH/D014406 Medical Subject Headings / 医学主题词表 LOOM
http://purl.obolibrary.org/obo/DOID_2123 BioAssay Ontology / 生物活性分析本体 LOOM
http://purl.obolibrary.org/obo/DOID_2123 Human Disease Ontology / 人类疾病本体 LOOM
http://purl.obolibrary.org/obo/DOID_2123 GenEpiO / 基因组流行病学本体 LOOM
http://purl.bioontology.org/ontology/ICD10CM/A21 International Classification of Diseases, Version 10 - Clinical Modification / 国际疾病分类,第10版-临床修改 LOOM
http://www.ebi.ac.uk/efo/EFO_1001444 Experimental Factor Ontology / 实验性因素本体 LOOM
http://purl.obolibrary.org/obo/MONDO_0018077 Mondo Disease Ontology / Mondo疾病本体 LOOM