| Preferred Name |
Tularemia |
| ID |
http://www.orpha.net/ORDO/Orphanet_3392 |
| definition |
A rare bacterial infectious disease caused by Francisella tularensis and characterized by six major clinical presentations: ulceroglandular, glandular, oropharyngeal, oculoglandular, pneumonic, or typhoidal, depending on the route of infection. Early flu-like symptoms are common to all forms and are accompanied/followed by either a skin inoculation ulcer with localized lymphadenopathy; isolated lymphadenopathy; chronic pharyngitis with cervical lymphadenopathy; conjunctivitis with localized lymphadenopathy; lung involvement; severe systemic disease with neurological symptoms. |
| definition_citation |
Orphanet |
| expertlink |
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=en&Expert=3392 |
| has_age_of_onset |
All ages |
| has_inheritance |
Not applicable |
| hasDbXref |
ICD-10:A21.1 ICD-10:A21.9 ICD-10:A21.0 ICD-11:1B94.Y UMLS:C0041351 ICD-10:A21.2 MeSH:D014406 ICD-10:A21.3 ICD-10:A21.8 ICD-10:A21.7 MedDRA:10045146 ICD-11:1B94 ICD-11:1B94.0 |
| label |
Tularemia |
| notation |
ORPHA:3392 |
| part_of | |
| prefixIRI |
ORDO:Orphanet_3392 |
| prefLabel |
Tularemia |
| present_in |
Slovenia AND has_annual_incidence_average_value : 0.01 AND has_annual_incidence_range : <1 / 1 000 000 France AND has_annual_incidence_average_value : 0.08 AND has_annual_incidence_range : <1 / 1 000 000 Latvia AND has_annual_incidence_average_value : 0.145 AND has_annual_incidence_range : 1-9 / 1 000 000 Bulgaria AND has_annual_incidence_average_value : 0.6 AND has_annual_incidence_range : 1-9 / 1 000 000 Europe AND has_annual_incidence_average_value : 0.2 AND has_annual_incidence_range : 1-9 / 1 000 000 Czech Republic AND has_annual_incidence_average_value : 1.27 AND has_annual_incidence_range : 1-9 / 100 000 Romania AND has_annual_incidence_average_value : 0.01 AND has_annual_incidence_range : <1 / 1 000 000 Norway AND has_annual_incidence_average_value : 1.83 AND has_annual_incidence_range : 1-9 / 100 000 Spain AND has_annual_incidence_average_value : 0.75 AND has_annual_incidence_range : 1-9 / 1 000 000 Lithuania AND has_annual_incidence_average_value : 0.07 AND has_annual_incidence_range : <1 / 1 000 000 Finland AND has_annual_incidence_average_value : 9.1 AND has_annual_incidence_range : 1-9 / 100 000 Netherlands AND has_annual_incidence_range : <1 / 1 000 000 Denmark AND has_annual_incidence_average_value : 0.05 AND has_annual_incidence_range : <1 / 1 000 000 Hungary AND has_annual_incidence_average_value : 0.5 AND has_annual_incidence_range : 1-9 / 1 000 000 Estonia AND has_annual_incidence_average_value : 0.075 AND has_annual_incidence_range : <1 / 1 000 000 Sweden AND has_annual_incidence_average_value : 4.0 AND has_annual_incidence_range : 1-9 / 100 000 Austria AND has_annual_incidence_average_value : 0.1 AND has_annual_incidence_range : 1-9 / 1 000 000 Europe AND has_point_prevalence_average_value : 2.0 AND has_point_prevalence_range : 1-9 / 100 000 Italy AND has_annual_incidence_average_value : 0.035 AND has_annual_incidence_range : <1 / 1 000 000 United Kingdom AND has_annual_incidence_range : <1 / 1 000 000 Switzerland AND has_annual_incidence_average_value : 0.25 AND has_annual_incidence_range : 1-9 / 1 000 000 Croatia AND has_annual_incidence_average_value : 0.3 AND has_annual_incidence_range : 1-9 / 1 000 000 Belgium AND has_annual_incidence_average_value : 0.005 AND has_annual_incidence_range : <1 / 1 000 000 Germany AND has_annual_incidence_average_value : 0.02 AND has_annual_incidence_range : <1 / 1 000 000 Poland AND has_annual_incidence_average_value : 0.01 AND has_annual_incidence_range : <1 / 1 000 000 Slovakia AND has_annual_incidence_average_value : 0.1 AND has_annual_incidence_range : 1-9 / 1 000 000 |
| treeView | |
| subClassOf |