Preferred Name |
granulomatosis with polyangiitis |
Synonyms |
Wegener granulomatosis, formerly |
Definitions |
An autoimmune disease that is characterized by necrotizing granulomatous inflammation of the upper and lower respiratory tract, glomerulonephritis, vasculitis, and the presence of antineutrophil cytoplasmatic autoantibodies (ANCAs) in patient sera, and is located_in lung, located_in kidney, located_in skin resulting from an autoimmune attack by antineutrophil cytoplasmic antibodies against small and medium-size blood vessels. |
ID |
http://purl.obolibrary.org/obo/DOID_12132 |
database_cross_reference |
OMIM:608710 ICD10CM:M31.3 ICD9CM:446.4 UMLS_CUI:C3495801 MESH:D014890 SNOMEDCT_US_2020_03_01:195353004 NCI:C3444 GARD:7880 |
has exact synonym |
Wegener granulomatosis, formerly Necrotizing respiratory granulomatosis |
id |
DOID:12132 |
in_subset | |
label |
granulomatosis with polyangiitis |
notation |
DOID:12132 |
prefLabel |
granulomatosis with polyangiitis |
textual definition |
An autoimmune disease that is characterized by necrotizing granulomatous inflammation of the upper and lower respiratory tract, glomerulonephritis, vasculitis, and the presence of antineutrophil cytoplasmatic autoantibodies (ANCAs) in patient sera, and is located_in lung, located_in kidney, located_in skin resulting from an autoimmune attack by antineutrophil cytoplasmic antibodies against small and medium-size blood vessels. |
引自 | |
有_obo_命名空间 |
disease_ontology |
subClassOf |
http://purl.obolibrary.org/obo/DOID_37 http://purl.obolibrary.org/obo/DOID_850 |