loading...| Preferred Name |
Pemphigus vulgaris |
| ID |
http://www.orpha.net/ORDO/Orphanet_704 |
| definition |
A rare autoimmune bullous skin diseases characterized by painful, flaccid blisters and erosions of the oral mucosa, predominantly involving the buccal area, and with or without extension to the epidermis. Mucosa of the larynx, oesophagus, conjunctiva, nose, genitalia and anus, are less frequently affected. |
| definition_citation |
Orphanet |
| expertlink |
https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=en&Expert=704 |
| has_age_of_onset |
Adult Elderly Childhood |
| has_inheritance |
Not applicable |
| hasDbXref |
ICD-10:L10.0 MedDRA:10052802 OMIM:169610 ICD-11:EB40.0 UMLS:C0030809 |
| label |
Pemphigus vulgaris |
| notation |
ORPHA:704 |
| part_of | |
| prefixIRI |
ORDO:Orphanet_704 |
| prefLabel |
Pemphigus vulgaris |
| present_in |
France AND has_annual_incidence_average_value : 0.13 AND has_annual_incidence_range : 1-9 / 1 000 000 Bulgaria AND has_annual_incidence_average_value : 0.47 AND has_annual_incidence_range : 1-9 / 1 000 000 Germany AND has_point_prevalence_average_value : 9.482 AND has_point_prevalence_range : 1-9 / 100 000 United Kingdom AND has_annual_incidence_average_value : 0.7 AND has_annual_incidence_range : 1-9 / 1 000 000 Europe AND has_point_prevalence_average_value : 18.0 AND has_point_prevalence_range : 1-5 / 10 000 Finland AND has_annual_incidence_average_value : 0.076 AND has_annual_incidence_range : <1 / 1 000 000 Tunisia AND has_annual_incidence_average_value : 0.25 AND has_annual_incidence_range : 1-9 / 1 000 000 United States AND has_annual_incidence_average_value : 0.42 AND has_annual_incidence_range : 1-9 / 1 000 000 |
| treeView | |
| subClassOf |