Preferred Name

Hepatic veno-occlusive disease

ID

http://www.orpha.net/ORDO/Orphanet_890

alternative_term

Sinusoidal obstruction syndrome

definition

A rare vascular liver disease characterized by toxic injury to the hepatic sinusoidal capillaries that leads to obstruction of the small hepatic veins and sinusoids. Clinical manifestations include painful hepatomegaly, jaundice, and fluid retention that manifests by weight gain, edemas, and ascites.

definition_citation

Orphanet

expertlink

https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=en&Expert=890

has_age_of_onset

All ages

has_inheritance

Not applicable

hasDbXref

MeSH:D006504

UMLS:C0019156

ICD-10:K76.5

MedDRA:10047216

ICD-11:DB98.6

label

Hepatic veno-occlusive disease

notation

ORPHA:890

part_of

http://www.orpha.net/ORDO/Orphanet_101938

http://www.orpha.net/ORDO/Orphanet_506210

prefixIRI

ORDO:Orphanet_890

prefLabel

Hepatic veno-occlusive disease

present_in

Worldwide AND has_point_prevalence_range : Unknown

treeView

http://www.orpha.net/ORDO/Orphanet_101938

http://www.orpha.net/ORDO/Orphanet_506210

subClassOf

http://www.orpha.net/ORDO/Orphanet_377788

http://www.orpha.net/ORDO/Orphanet_557493

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