Medical Subject Headings / 医学主题词表

Last uploaded: September 7, 2023
Preferred Name

Moyamoya Disease

Synonyms

Moya-Moya Disease

Definitions

A noninflammatory, progressive occlusion of the intracranial CAROTID ARTERIES and the formation of netlike collateral arteries arising from the CIRCLE OF WILLIS. Cerebral angiogram shows the puff-of-smoke (moyamoya) collaterals at the base of the brain. It is characterized by endothelial HYPERPLASIA and FIBROSIS with thickening of arterial walls. This disease primarily affects children but can also occur in adults.

ID

http://purl.bioontology.org/ontology/MESH/D009072

altLabel

Moya-Moya Disease

Moyamoya Syndrome

Progressive Intracranial Occlusive Arteropathy (Moyamoya)

Disease, Primary Moyamoya

Classic Moyamoya Disease

Moyamoya Disease, Secondary

Secondary Moyamoya Disease

Primary Moyamoya Disease

Moya Moya Disease

Moyamoya Diseases, Primary

Disease, Classic Moyamoya

Cerebrovascular Moyamoya Disease

Moyamoya Disease, Primary

Primary Moyamoya Diseases

Disease, Moya-Moya

Moyamoya Disease, Classic

AQL

BL CF CI CL CN CO DG DH DI DT EC EH EM EN EP ET GE HI IM ME MI MO NU PA PC PP PS PX RH RT SU TH UR VE VI

cui

C0751323

C0026654

C0751322

DC

1

definition

A noninflammatory, progressive occlusion of the intracranial CAROTID ARTERIES and the formation of netlike collateral arteries arising from the CIRCLE OF WILLIS. Cerebral angiogram shows the puff-of-smoke (moyamoya) collaterals at the base of the brain. It is characterized by endothelial HYPERPLASIA and FIBROSIS with thickening of arterial walls. This disease primarily affects children but can also occur in adults.

DX

19910101

HN

1991(1978)

Inverse of AQ

http://purl.bioontology.org/ontology/MESH/Q000401

http://purl.bioontology.org/ontology/MESH/Q000150

http://purl.bioontology.org/ontology/MESH/Q000188

http://purl.bioontology.org/ontology/MESH/Q000517

http://purl.bioontology.org/ontology/MESH/Q000201

http://purl.bioontology.org/ontology/MESH/Q000145

http://purl.bioontology.org/ontology/MESH/Q000503

http://purl.bioontology.org/ontology/MESH/Q000453

http://purl.bioontology.org/ontology/MESH/Q000208

http://purl.bioontology.org/ontology/MESH/Q000134

http://purl.bioontology.org/ontology/MESH/Q000821

http://purl.bioontology.org/ontology/MESH/Q000382

http://purl.bioontology.org/ontology/MESH/Q000601

http://purl.bioontology.org/ontology/MESH/Q000235

http://purl.bioontology.org/ontology/MESH/Q000523

http://purl.bioontology.org/ontology/MESH/Q000276

http://purl.bioontology.org/ontology/MESH/Q000191

http://purl.bioontology.org/ontology/MESH/Q000652

http://purl.bioontology.org/ontology/MESH/Q000662

http://purl.bioontology.org/ontology/MESH/Q000151

http://purl.bioontology.org/ontology/MESH/Q000628

http://purl.bioontology.org/ontology/MESH/Q000196

http://purl.bioontology.org/ontology/MESH/Q000534

http://purl.bioontology.org/ontology/MESH/Q000266

http://purl.bioontology.org/ontology/MESH/Q000532

http://purl.bioontology.org/ontology/MESH/Q000139

http://purl.bioontology.org/ontology/MESH/Q000378

http://purl.bioontology.org/ontology/MESH/Q000175

http://purl.bioontology.org/ontology/MESH/Q000000981

http://purl.bioontology.org/ontology/MESH/Q000097

http://purl.bioontology.org/ontology/MESH/Q000473

http://purl.bioontology.org/ontology/MESH/Q000451

http://purl.bioontology.org/ontology/MESH/Q000209

http://purl.bioontology.org/ontology/MESH/Q000178

http://purl.bioontology.org/ontology/MESH/Q000469

Machine permutation

1991; see ARTERIAL OCCLUSIVE DISEASES 1978-1990

Mapped from

http://purl.bioontology.org/ontology/MESH/C536993

http://purl.bioontology.org/ontology/MESH/C536991

http://purl.bioontology.org/ontology/MESH/C536992

MDA

19770427

MMR

20120703

MN

C14.907.253.560.200.737

C10.228.140.300.510.200.737

C14.907.137.615

C14.907.253.123.620

C10.228.140.300.200.600

notation

D009072

prefLabel

Moyamoya Disease

TERMUI

T369519

T369520

T369517

T027090

T369518

T027091

T369516

T369521

TH

NLM (1978)

NLM (2000)

ORD (2010)

OMIM (2013)

NLM (1999)

tui

T047

subClassOf

http://purl.bioontology.org/ontology/MESH/D002539

http://purl.bioontology.org/ontology/MESH/D002340

http://purl.bioontology.org/ontology/MESH/D001157

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Delete Mapping To Ontology Source
http://purl.bioontology.org/ontology/OMIM/MTHU037610 Online Mendelian Inheritance in Man / 在线人类孟德尔遗传数据库 CUI
http://purl.obolibrary.org/obo/MONDO_0016820 Mondo Disease Ontology / Mondo疾病本体 LOOM
http://purl.obolibrary.org/obo/MONDO_0016820 Experimental Factor Ontology / 实验性因素本体 LOOM
http://purl.bmicc.cn/ontology/ICD10CN/I67.5 《国际疾病分类》第10版中文版 / International Classification of Diseases, 10th Edition, China CUI
http://purl.bioontology.org/ontology/OMIM/MTHU023633 Online Mendelian Inheritance in Man / 在线人类孟德尔遗传数据库 CUI
http://purl.bioontology.org/ontology/OMIM/MTHU023633 Online Mendelian Inheritance in Man / 在线人类孟德尔遗传数据库 LOOM
http://purl.bioontology.org/ontology/ICD10CM/I67.5 International Classification of Diseases, Version 10 - Clinical Modification / 国际疾病分类,第10版-临床修改 CUI
http://purl.bioontology.org/ontology/ICD10CM/I67.5 International Classification of Diseases, Version 10 - Clinical Modification / 国际疾病分类,第10版-临床修改 LOOM
http://purl.bioontology.org/ontology/OMIM/MTHU041200 Online Mendelian Inheritance in Man / 在线人类孟德尔遗传数据库 CUI
http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C84895 National Cancer Institute Thesaurus / 美国国家癌症研究所词典 LOOM
http://www.orpha.net/ORDO/Orphanet_2573 Orphanet Rare Disease Ontology / Orphanet罕见病本体 LOOM
http://purl.obolibrary.org/obo/DOID_13099 BioAssay Ontology / 生物活性分析本体 LOOM
http://purl.obolibrary.org/obo/DOID_13099 Human Disease Ontology / 人类疾病本体 LOOM
http://purl.bioontology.org/ontology/ICD10/I67.5 International Classification of Diseases, Version 10 / 《国际疾病分类》第10版 CUI
http://purl.bioontology.org/ontology/ICD10/I67.5 International Classification of Diseases, Version 10 / 《国际疾病分类》第10版 LOOM