loading...| Preferred Name |
Double outlet right ventricle |
| Synonyms |
Double-outlet right ventricle DORV |
| Definitions |
During the development of the heart, the outflow tract initially connects exclusively with the primitive right ventricle and must undergo extensive remodelling to divide into a separate pulmonary artery and aorta; subsequently, there is continued remodelling to establish direct continuity from the left ventricle to the aorta. DORV encompasses a wide spectrum of anatomic arrangements and pathophysiologic disturbances. At one end of the spectrum, it mimics tetralogy of Fallot in the presence of pulmonary stenosis, or a large ventricular septal defect (VSD) in the absence of such stenosis. At the other end of the spectrum, it behaves like transposition of the great arteries with a VSD. Double outlet right ventricle (DORV) is a type of ventriculoarterial connection in which both great vessels arise entirely or predominantly from the right ventricle. |
| ID |
http://purl.obolibrary.org/obo/HP_0001719 |
| comment |
During the development of the heart, the outflow tract initially connects exclusively with the primitive right ventricle and must undergo extensive remodelling to divide into a separate pulmonary artery and aorta; subsequently, there is continued remodelling to establish direct continuity from the left ventricle to the aorta. DORV encompasses a wide spectrum of anatomic arrangements and pathophysiologic disturbances. At one end of the spectrum, it mimics tetralogy of Fallot in the presence of pulmonary stenosis, or a large ventricular septal defect (VSD) in the absence of such stenosis. At the other end of the spectrum, it behaves like transposition of the great arteries with a VSD. |
| database_cross_reference |
SNOMEDCT_US:7484005 Fyler:600 UMLS:C0013069 MSH:D004310 Fyler:606 |
| definition |
Double outlet right ventricle (DORV) is a type of ventriculoarterial connection in which both great vessels arise entirely or predominantly from the right ventricle. |
| has_exact_synonym |
Double-outlet right ventricle DORV |
| has_obo_namespace |
human_phenotype |
| id |
HP:0001719 |
| label |
Double outlet right ventricle |
| notation |
HP:0001719 |
| prefLabel |
Double outlet right ventricle |
| treeView | |
| subClassOf |