Preferred Name

Pyoderma gangrenosum

ID

http://www.orpha.net/ORDO/Orphanet_48104

definition

Pyoderma gangrenosum (PG) is a primarily sterile inflammatory neutrophilic dermatosis characterized by recurrent cutaneous ulcerations with a mucopurulent or hemorrhagic exudate.

definition_citation

Orphanet

expertlink

https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=en&Expert=48104

has_age_of_onset

Adult

Adolescent

Elderly

Childhood

has_inheritance

Unknown

hasDbXref

ICD-10:L88

UMLS:C0085652

MeSH:D017511

ICD-11:EB21

MedDRA:10037635

label

Pyoderma gangrenosum

notation

ORPHA:48104

part_of

http://www.orpha.net/ORDO/Orphanet_290842

http://www.orpha.net/ORDO/Orphanet_324927

prefixIRI

ORDO:Orphanet_48104

prefLabel

Pyoderma gangrenosum

present_in

Worldwide AND has_point_prevalence_range : Unknown

Italy AND has_annual_incidence_average_value : 0.517 AND has_annual_incidence_range : 1-9 / 1 000 000

Spain AND has_annual_incidence_average_value : 0.33 AND has_annual_incidence_range : 1-9 / 1 000 000

Worldwide AND has_annual_incidence_average_value : 0.74 AND has_annual_incidence_range : 1-9 / 1 000 000

United Kingdom AND has_annual_incidence_average_value : 0.91 AND has_annual_incidence_range : 1-9 / 1 000 000

United States AND has_annual_incidence_average_value : 1.0 AND has_annual_incidence_range : 1-9 / 100 000

treeView

http://www.orpha.net/ORDO/Orphanet_290842

http://www.orpha.net/ORDO/Orphanet_324927

subClassOf

http://www.orpha.net/ORDO/Orphanet_377788

http://www.orpha.net/ORDO/Orphanet_557493

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Delete Mapping To Ontology Source
http://purl.bioontology.org/ontology/OMIM/MTHU038674 Online Mendelian Inheritance in Man / 在线人类孟德尔遗传数据库 LOOM
http://purl.obolibrary.org/obo/DOID_8553 BioAssay Ontology / 生物活性分析本体 LOOM
http://purl.obolibrary.org/obo/DOID_8553 Human Disease Ontology / 人类疾病本体 LOOM
http://purl.bioontology.org/ontology/ICD10CM/L88 International Classification of Diseases, Version 10 - Clinical Modification / 国际疾病分类,第10版-临床修改 LOOM
http://purl.bmicc.cn/ontology/ICD11CN/EB21 《国际疾病分类》第11版中文版 / International Classification of Diseases, 11th Edition, China LOOM
http://purl.bioontology.org/ontology/MESH/D017511 Medical Subject Headings / 医学主题词表 LOOM
http://purl.bioontology.org/ontology/ICD10/L88 International Classification of Diseases, Version 10 / 《国际疾病分类》第10版 LOOM
http://purl.obolibrary.org/obo/MONDO_0018824 Mondo Disease Ontology / Mondo疾病本体 LOOM
http://www.ebi.ac.uk/efo/EFO_0006835 Experimental Factor Ontology / 实验性因素本体 LOOM
http://purl.obolibrary.org/obo/HP_0025452 Human Phenotype Ontology / 人类表型本体 LOOM