Medical Subject Headings / 医学主题词表

Last uploaded: September 7, 2023
Preferred Name

Frontotemporal Dementia

Synonyms

GRN-Related Frontotemporal Dementias

Definitions

The most common clinical form of FRONTOTEMPORAL LOBAR DEGENERATION, this dementia presents with personality and behavioral changes often associated with disinhibition, apathy, and lack of insight.

ID

http://purl.bioontology.org/ontology/MESH/D057180

altLabel

GRN-Related Frontotemporal Dementias

Frontotemporal Dementias, Ubiquitin-Positive

Multiple System Tauopathy with Presenile Dementia

Familial Pick's Disease

Lobe Dementia, Frontotemporal

Dementia, Frontotemporal

Hereditary Dysphasic Disinhibition Dementia

FTLD-TDP

Pick's Diseases, Familial

Frontotemporal Dementia with Parkinsonism-17

Disease, Wilhelmsen-Lynch

Dementias, Frontotemporal Lobe

Dementia, Frontotemporal Lobe (FLDEM)

FTLD-17 GRN

Disinhibition-Dementia-Parkinsonism-Amytrophy Complices

DDPAC

Disinhibition-Dementia-Parkinsonism-Amytrophy Complex

GRN Related Frontotemporal Dementia

Dementia, Hereditary Dysphasic Disinhibition

GRN-Related Frontotemporal Dementia

Disinhibition-Dementia-Parkinsonism-Amyotrophy Complex

Dementias, Ubiquitin-Positive Frontotemporal

FTLD with TDP 43 Pathology

Dementia, Semantic

Wilhelmsen-Lynch Disease

Frontotemporal Dementia, Ubiquitin-Positive

Complex, Disinhibition-Dementia-Parkinsonism-Amyotrophy

Ubiquitin-Positive Frontotemporal Dementia

Dementias, Semantic

Dementia, Frontotemporal, with Parkinsonism

Dementias, Frontotemporal Lobe (FLDEM)

Disease, Familial Pick's

Disinhibition Dementia Parkinsonism Amyotrophy Complex

Frontotemporal Lobe Dementia (FLDEM)

FTD-GRN

Complex, Disinhibition-Dementia-Parkinsonism-Amytrophy

Disinhibition-Dementia-Parkinsonism-Amyotrophy Complices

Frontotemporal Dementia with Parkinsonism

Complices, Disinhibition-Dementia-Parkinsonism-Amyotrophy

Frontotemporal Lobar Degeneration With Ubiquitin-Positive Inclusions

FTDP-17

Frontotemporal Lobe Dementia

Familial Pick Disease

Dementia, Ubiquitin-Positive Frontotemporal

Disinhibition Dementia Parkinsonism Amytrophy Complex

Diseases, Wilhelmsen-Lynch

HDDD2

Dementia, GRN-Related Frontotemporal

Frontotemporal Lobe Dementias (FLDEM)

Frontotemporal Lobe Dementias

HDDD1

Lobe Dementias, Frontotemporal

Frontotemporal Dementia, GRN-Related

Dementias, Frontotemporal

Dementia, Frontotemporal Lobe

Wilhelmsen Lynch Disease

Wilhelmsen-Lynch Diseases

Semantic Dementias

Semantic Dementia

Frontotemporal Dementias

Complices, Disinhibition-Dementia-Parkinsonism-Amytrophy

Dementias, GRN-Related Frontotemporal

Familial Picks Disease

Frontotemporal Dementia, Ubiquitin Positive

Frontotemporal Dementia with Parkinsonism 17

Ubiquitin-Positive Frontotemporal Dementias

Frontotemporal Lobar Degeneration With Ubiquitin Positive Inclusions

Frontotemporal Dementias, GRN-Related

Familial Pick's Diseases

FTLD with TDP-43 Pathology

FTD-PGRN

Pick's Disease, Familial

Diseases, Familial Pick's

AQL

BL CF CI CL CO DG DH DI DT EC EH EN EP ET GE HI IM ME MI MO NU PA PC PP PS PX RH SU TH UR VI

cui

C0338451

C0338462

DC

1

definition

The most common clinical form of FRONTOTEMPORAL LOBAR DEGENERATION, this dementia presents with personality and behavioral changes often associated with disinhibition, apathy, and lack of insight.

DX

20100101

HN

2010

Inverse of AQ

http://purl.bioontology.org/ontology/MESH/Q000401

http://purl.bioontology.org/ontology/MESH/Q000150

http://purl.bioontology.org/ontology/MESH/Q000188

http://purl.bioontology.org/ontology/MESH/Q000517

http://purl.bioontology.org/ontology/MESH/Q000201

http://purl.bioontology.org/ontology/MESH/Q000145

http://purl.bioontology.org/ontology/MESH/Q000503

http://purl.bioontology.org/ontology/MESH/Q000453

http://purl.bioontology.org/ontology/MESH/Q000208

http://purl.bioontology.org/ontology/MESH/Q000134

http://purl.bioontology.org/ontology/MESH/Q000821

http://purl.bioontology.org/ontology/MESH/Q000382

http://purl.bioontology.org/ontology/MESH/Q000601

http://purl.bioontology.org/ontology/MESH/Q000235

http://purl.bioontology.org/ontology/MESH/Q000523

http://purl.bioontology.org/ontology/MESH/Q000276

http://purl.bioontology.org/ontology/MESH/Q000191

http://purl.bioontology.org/ontology/MESH/Q000652

http://purl.bioontology.org/ontology/MESH/Q000628

http://purl.bioontology.org/ontology/MESH/Q000534

http://purl.bioontology.org/ontology/MESH/Q000266

http://purl.bioontology.org/ontology/MESH/Q000139

http://purl.bioontology.org/ontology/MESH/Q000378

http://purl.bioontology.org/ontology/MESH/Q000175

http://purl.bioontology.org/ontology/MESH/Q000000981

http://purl.bioontology.org/ontology/MESH/Q000097

http://purl.bioontology.org/ontology/MESH/Q000473

http://purl.bioontology.org/ontology/MESH/Q000451

http://purl.bioontology.org/ontology/MESH/Q000209

http://purl.bioontology.org/ontology/MESH/Q000178

http://purl.bioontology.org/ontology/MESH/Q000469

Machine permutation

2010

Mapped from

http://purl.bioontology.org/ontology/MESH/C567699

http://purl.bioontology.org/ontology/MESH/C563476

http://purl.bioontology.org/ontology/MESH/C566288

http://purl.bioontology.org/ontology/MESH/C579991

http://purl.bioontology.org/ontology/MESH/C563003

MDA

20090706

MMR

20150623

MN

C18.452.845.800.300.299

C10.574.950.300.299

F03.615.400.380.299

C10.228.140.380.266.299

notation

D057180

prefLabel

Frontotemporal Dementia

TERMUI

T843043

T812307

T843512

T749906

T812309

T841458

T843466

T749903

T749907

T843511

T843508

T749901

T843509

T812698

T367225

T841457

T749900

T749899

T749902

T812308

T843465

T841455

T812640

T843042

T843510

T841555

T843467

TH

NLM (2000)

NLM (2010)

NLM (2014)

ORD (2010)

OMIM (2013)

GHR (2014)

tui

T048

T047

subClassOf

http://purl.bioontology.org/ontology/MESH/D057174

Delete Subject Author Type Created
No notes to display
Create New Mapping

Delete Mapping To Ontology Source
http://www.orpha.net/ORDO/Orphanet_282 Orphanet Rare Disease Ontology / Orphanet罕见病本体 LOOM
http://purl.bioontology.org/ontology/OMIM/104311 Online Mendelian Inheritance in Man / 在线人类孟德尔遗传数据库 CUI
http://purl.bioontology.org/ontology/ICD10CM/G31.0 International Classification of Diseases, Version 10 - Clinical Modification / 国际疾病分类,第10版-临床修改 CUI
http://purl.bioontology.org/ontology/ICD10CM/G31.0 International Classification of Diseases, Version 10 - Clinical Modification / 国际疾病分类,第10版-临床修改 LOOM
http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C84719 National Cancer Institute Thesaurus / 美国国家癌症研究所词典 LOOM
http://purl.bioontology.org/ontology/OMIM/157140 Online Mendelian Inheritance in Man / 在线人类孟德尔遗传数据库 CUI
http://purl.bioontology.org/ontology/OMIM/MTHU003256 Online Mendelian Inheritance in Man / 在线人类孟德尔遗传数据库 CUI
http://purl.bioontology.org/ontology/OMIM/MTHU003256 Online Mendelian Inheritance in Man / 在线人类孟德尔遗传数据库 LOOM
http://purl.bioontology.org/ontology/OMIM/138945 Online Mendelian Inheritance in Man / 在线人类孟德尔遗传数据库 CUI
http://purl.obolibrary.org/obo/DOID_9255 Coronavirus Infectious Disease Ontology / 冠状病毒感染性疾病本体 LOOM
http://purl.obolibrary.org/obo/DOID_9255 Human Disease Ontology / 人类疾病本体 LOOM
http://purl.obolibrary.org/obo/HP_0002145 Human Phenotype Ontology / 人类表型本体 LOOM
http://purl.obolibrary.org/obo/MONDO_0017276 Mondo Disease Ontology / Mondo疾病本体 LOOM
http://purl.obolibrary.org/obo/MONDO_0017276 Experimental Factor Ontology / 实验性因素本体 LOOM
http://purl.bmicc.cn/ontology/ICD11CN/6D83 《国际疾病分类》第11版中文版 / International Classification of Diseases, 11th Edition, China LOOM
http://purl.bioontology.org/ontology/OMIM/600274 Online Mendelian Inheritance in Man / 在线人类孟德尔遗传数据库 CUI
http://purl.bioontology.org/ontology/OMIM/600274 Online Mendelian Inheritance in Man / 在线人类孟德尔遗传数据库 LOOM