| Preferred Name |
Frontotemporal Dementia |
| Synonyms |
GRN-Related Frontotemporal Dementias |
| Definitions |
The most common clinical form of FRONTOTEMPORAL LOBAR DEGENERATION, this dementia presents with personality and behavioral changes often associated with disinhibition, apathy, and lack of insight. |
| ID |
http://purl.bioontology.org/ontology/MESH/D057180 |
| altLabel |
GRN-Related Frontotemporal Dementias Frontotemporal Dementias, Ubiquitin-Positive Multiple System Tauopathy with Presenile Dementia Familial Pick's Disease Lobe Dementia, Frontotemporal Dementia, Frontotemporal Hereditary Dysphasic Disinhibition Dementia FTLD-TDP Pick's Diseases, Familial Frontotemporal Dementia with Parkinsonism-17 Disease, Wilhelmsen-Lynch Dementias, Frontotemporal Lobe Dementia, Frontotemporal Lobe (FLDEM) FTLD-17 GRN Disinhibition-Dementia-Parkinsonism-Amytrophy Complices DDPAC Disinhibition-Dementia-Parkinsonism-Amytrophy Complex GRN Related Frontotemporal Dementia Dementia, Hereditary Dysphasic Disinhibition GRN-Related Frontotemporal Dementia Disinhibition-Dementia-Parkinsonism-Amyotrophy Complex Dementias, Ubiquitin-Positive Frontotemporal FTLD with TDP 43 Pathology Dementia, Semantic Wilhelmsen-Lynch Disease Frontotemporal Dementia, Ubiquitin-Positive Complex, Disinhibition-Dementia-Parkinsonism-Amyotrophy Ubiquitin-Positive Frontotemporal Dementia Dementias, Semantic Dementia, Frontotemporal, with Parkinsonism Dementias, Frontotemporal Lobe (FLDEM) Disease, Familial Pick's Disinhibition Dementia Parkinsonism Amyotrophy Complex Frontotemporal Lobe Dementia (FLDEM) FTD-GRN Complex, Disinhibition-Dementia-Parkinsonism-Amytrophy Disinhibition-Dementia-Parkinsonism-Amyotrophy Complices Frontotemporal Dementia with Parkinsonism Complices, Disinhibition-Dementia-Parkinsonism-Amyotrophy Frontotemporal Lobar Degeneration With Ubiquitin-Positive Inclusions FTDP-17 Frontotemporal Lobe Dementia Familial Pick Disease Dementia, Ubiquitin-Positive Frontotemporal Disinhibition Dementia Parkinsonism Amytrophy Complex Diseases, Wilhelmsen-Lynch HDDD2 Dementia, GRN-Related Frontotemporal Frontotemporal Lobe Dementias (FLDEM) Frontotemporal Lobe Dementias HDDD1 Lobe Dementias, Frontotemporal Frontotemporal Dementia, GRN-Related Dementias, Frontotemporal Dementia, Frontotemporal Lobe Wilhelmsen Lynch Disease Wilhelmsen-Lynch Diseases Semantic Dementias Semantic Dementia Frontotemporal Dementias Complices, Disinhibition-Dementia-Parkinsonism-Amytrophy Dementias, GRN-Related Frontotemporal Familial Picks Disease Frontotemporal Dementia, Ubiquitin Positive Frontotemporal Dementia with Parkinsonism 17 Ubiquitin-Positive Frontotemporal Dementias Frontotemporal Lobar Degeneration With Ubiquitin Positive Inclusions Frontotemporal Dementias, GRN-Related Familial Pick's Diseases FTLD with TDP-43 Pathology FTD-PGRN Pick's Disease, Familial Diseases, Familial Pick's |
| AQL |
BL CF CI CL CO DG DH DI DT EC EH EN EP ET GE HI IM ME MI MO NU PA PC PP PS PX RH SU TH UR VI |
| cui |
C0338451 C0338462 |
| DC |
1 |
| definition |
The most common clinical form of FRONTOTEMPORAL LOBAR DEGENERATION, this dementia presents with personality and behavioral changes often associated with disinhibition, apathy, and lack of insight. |
| DX |
20100101 |
| HN |
2010 |
| Inverse of AQ |
http://purl.bioontology.org/ontology/MESH/Q000401 http://purl.bioontology.org/ontology/MESH/Q000150 http://purl.bioontology.org/ontology/MESH/Q000188 http://purl.bioontology.org/ontology/MESH/Q000517 http://purl.bioontology.org/ontology/MESH/Q000201 http://purl.bioontology.org/ontology/MESH/Q000145 http://purl.bioontology.org/ontology/MESH/Q000503 http://purl.bioontology.org/ontology/MESH/Q000453 http://purl.bioontology.org/ontology/MESH/Q000208 http://purl.bioontology.org/ontology/MESH/Q000134 http://purl.bioontology.org/ontology/MESH/Q000821 http://purl.bioontology.org/ontology/MESH/Q000382 http://purl.bioontology.org/ontology/MESH/Q000601 http://purl.bioontology.org/ontology/MESH/Q000235 http://purl.bioontology.org/ontology/MESH/Q000523 http://purl.bioontology.org/ontology/MESH/Q000276 http://purl.bioontology.org/ontology/MESH/Q000191 http://purl.bioontology.org/ontology/MESH/Q000652 http://purl.bioontology.org/ontology/MESH/Q000628 http://purl.bioontology.org/ontology/MESH/Q000534 http://purl.bioontology.org/ontology/MESH/Q000266 http://purl.bioontology.org/ontology/MESH/Q000139 http://purl.bioontology.org/ontology/MESH/Q000378 http://purl.bioontology.org/ontology/MESH/Q000175 http://purl.bioontology.org/ontology/MESH/Q000000981 http://purl.bioontology.org/ontology/MESH/Q000097 http://purl.bioontology.org/ontology/MESH/Q000473 http://purl.bioontology.org/ontology/MESH/Q000451 http://purl.bioontology.org/ontology/MESH/Q000209 |
| Machine permutation |
2010 |
| Mapped from |
http://purl.bioontology.org/ontology/MESH/C567699 http://purl.bioontology.org/ontology/MESH/C563476 http://purl.bioontology.org/ontology/MESH/C566288 |
| MDA |
20090706 |
| MMR |
20150623 |
| MN |
C18.452.845.800.300.299 C10.574.950.300.299 F03.615.400.380.299 C10.228.140.380.266.299 |
| notation |
D057180 |
| prefLabel |
Frontotemporal Dementia |
| TERMUI |
T843043 T812307 T843512 T749906 T812309 T841458 T843466 T749903 T749907 T843511 T843508 T749901 T843509 T812698 T367225 T841457 T749900 T749899 T749902 T812308 T843465 T841455 T812640 T843042 T843510 T841555 T843467 |
| TH |
NLM (2000) NLM (2010) NLM (2014) ORD (2010) OMIM (2013) GHR (2014) |
| tui |
T048 T047 |
| subClassOf |